NCT07227207PHASE1, PHASE2Recruiting
A Study of TSRA-196 in Adults With PiZZ Alpha-1 Antitrypsin Deficiency (AATD)
Tessera Therapeutics, Inc.
Start Date
4/21/2026
Completion Date
3/1/2029
Summary
This is a Phase 1/2, open-label, multi-center, dose escalation (Part 1), dose expansion (Part 2), and single repeat dose (Part 3) study to evaluate the safety, tolerability, efficacy, and PK/PD parameters of TSRA-196 in adults with the PiZZ genotype who have lung and/or liver disease associated with severe alpha-1 antitrypsin deficiency (AATD)
Eligibility Criteria
Age Range: 18 years to 70 years
Inclusion Criteria:
* Males or females who are 18 to 70 years of age, inclusive, at the time of signing the informed consent
* Body mass index of 18 to 37 kg/m2, inclusive
* Confirmed diagnosis of AATD and PiZZ genotype
* At least one previous measure of blood total AAT level \<11 µmol/L
* Nonsmoker for at least 6 months before screening and must remain nonsmoking for the entire study duration
* Either AAT treatment-naïve or washed out of all investigational or approved treatments that modify AAT levels for 5 half-lives or at least 4 weeks, whichever is longer, before TSRA-196 administration
Parts 1A and 2A (AATD lung disease with no or minimal liver fibrosis)
* Clinically significant lung disease, defined as 1) evidence of emphysema or bronchiectasis by computed tomography or 2) DLCO \<70% of the predicted value or 3) ppFEV1 \<80%
* ppFEV1 ≥35%
* METAVIR fibrosis score F0 or F1 confirmed by liver biopsy at screening, or a liver stiffness measure by FibroScan ≤7 kPa at screening
* FIB-4 index score ≤3.25 at screening
* ALT and/or AST \<ULN at screening
Parts 1B and 2B (AATD liver disease with significant or severe liver fibrosis, with or without AATD lung disease)
* METAVIR fibrosis score F2 or F3 confirmed by liver biopsy at screening. A liver biopsy conducted within 12 months before screening is acceptable as a substitute.
* Liver stiffness measure by FibroScan \>7 and ≤15 kPa at screening
* ALT and/or AST \<2 x ULN at screening
Exclusion Criteria:
* Presence of genetic variation in SERPINA1 gene that may disrupt the function of TSRA-196, determined by screening genotyping
* History of liver disease unrelated to AATD, or history of or clinical signs of cirrhosis
* Significant lung disease not attributable to manifestations of AATD, as determined by the investigator
* History of one or more hospitalizations due to severe exacerbation of underlying lung disease during the year before screening or received IV antibiotics for treatment of a pulmonary infection within 6 months before screening
* Unstable AATD-related COPD, as determined by the investigator, or severe bronchiectasis
* Lung volume reduction surgery within 1 year before screening or plan to receive lung volume reduction surgery during the study period
* Documented chronic need for positive airway pressure therapy beyond nocturnal use
* Seropositive for human immunodeficiency virus (HIV) (HIV-1 or HIV-2)
* Seropositive for hepatitis B (hepatitis B surface antigen \[HBsAg\] or hepatitis B core antibody \[HBcAb\] positive) with detectable HBV DNA
* Hepatitis C virus (HCV) RNA positive at screening (Parts 1A and 2A), or HCV RNA positive and/or HCV antibody positive at screening (Parts 1B and 2B)
* Has received an organ transplant or is on a waiting list for an organ transplant
* Prior treatment with gene therapy using viral vectors or intended to permanently change the patient's DNA
* Any investigational products within 30 days before dosing or plan to take an investigational product before the end of study
Interventions
DRUG
TSRA-196
Conditions
Alpha-1 Antitrypsin Deficiency (AATD)
Locations
Clinical Study Center
Boston, Massachusetts 02118
United States
Clinical Study Center
Charleston, South Carolina 29425
United States
Clinical Study Center
Fitzroy, Victoria
Australia